Carcinoid tumor

What causes carcinoid tumors?

The cause of carcinoid tumors is currently unknown. There are some unavoidable risk factors that may increase a person's risk of developing the tumor. It is important to note that people with several risk factors may never develop cancer, while others with no risk factors may develop cancer. Possible risk factors for carcinoid tumors include:

Last updated on 05-01-20

Can an individual be predisposed to develop a carcinoid tumor?

Carcinoid tumors generally have been considered to be sporadic, except for a small proportion which occur as a part of multiple endocrine neoplasia (MEN) syndromes. Carcinoid tumors most notably may occur in MEN1, and occasionally in MEN2. These conditions are caused by mutations in the MEN1 and RET genes, respectively, and most cases are considered to have an autosomal dominant pattern of inheritance. When associated with these familial syndromes, carcinoids are more likely to develop in the foregut, especially in the thymus and lung.

It has been reported that even when a carcinoid tumor does not appear to be associated with MEN, there does appear to be an increased risk for developing a carcinoid tumor among first-degree relatives; this suggests that some carcinoid tumors may be familial. However, little data are available on the percentage of individuals with a carcinoid tumor that have a family history of carcinoid tumors.

Last updated on 05-01-20

Name: American Cancer Society 250 Williams Street NW
Atlanta, GA, 30329, United States
Toll Free: 1-800-227-2345 Url:
Name: Carcinoid Cancer Foundation 333 Mamaroneck Avenue Suite 492
White Plains, NY, 10605 , United States
Phone: +1-914-683-1001 Toll Free: 1-888-722-3132 Fax : +1-914-683-5919 Url:
Name: Neuroendocrine Tumor Research Foundation NETRF 321 Columbus Avenue, Suite 5R
Boston, MA, 02116 , United States
Phone: +1-617-946-1780 Email: Url:
Name: NET Patient Foundation UK and Ireland Holly House (2nd Floor) 74 Upper Holly Walk
Leamington Spa
Warwickshire, CV32 4JL, United Kingdom
Phone: 01926 883487 (General inquieries) Toll Free: 0800 434 6476 (Helpline) Email: Url:
Name: Carcinoid NeuroEndocrine Tumour Society Canada CNETS Canada 1608 Blakely Drive
Cornwall, Ontario, K6J 5P4, Canada
Phone: +1-416-628-3189 Toll Free: 1-844-628-6788 Email:, Url:
Name: Pancreatica Cancer Patients Alliance 312 Fountain Avenue
Pacific Grove, CA, 93950,
Phone: +1-831-658-0600 Email: Url:
Name: The Healing NET Foundation 200 Hill Avenue Suite 4
Nashville, TN, 37210, United States
Phone: 615-3696463 Email: Url:
Name: North American Neuroendocrine Tumor Society NANETS 136 Everett Road
Albany, NY, 12205, United States
Phone: (650) 762-6387 Email: Url:
Name: Neuroendocrine Cancer Awareness Network NCAN 3074 Brookchase Blvd
Fort Mill, SC, 29707, United States
Phone: 866-850-9555 Email:, Url:
Tebbi CK. Carcinoid Tumor Treatment & Management Medscape. 2014; Reference Link

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