Osteofibrous dysplasia

What is the prognosis for individuals with osteofibrous dysplasia?

The course of disease progression is variable. In some cases, the tumor grows at a moderate pace throughout childhood. In other cases, tumor growth is aggressive, resulting in bowing and deformity of the limb. Spontaneous resolution is also possible. Once the bone stops growing, the condition usually stabilizes or improves. If surgery is performed before the bone is done growing, recurrence is common (64-100%). Recurrence is unlikely after skeletal maturation. Malignant transformation has not been reported.

Last updated on 05-01-20

Tis JE. Benign bone tumors in children and adolescents: An overview UpToDate. June 26, 2015; Reference Link

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