Are oligodendrogliomas rare?

In the United States, a rare disease is defined as a condition that affects fewer than 200,000 people. This definition was created by Congress in the Orphan Drug Act of 1983. Other countries have their own official definitions of a rare disease. In Europe, a disease is defined as rare when it affects fewer than 1 in 2,000 people.

According to Orphanet, the annual incidence can be estimated at around one new case per 100,000 individuals per year. The prevalence is estimated at 1/300,000, but this may be an underestimate, as the condition is likely under-diagnosed.

The Central Brain Tumor Registry of the United States (CBTRUS) was formed in 1992 through the American Brain Tumor Association as a resource for epidemiologic data on primary brain tumors. Primary brain tumors represent only 2% of all cancers, with 35,000 new cases diagnosed each year in the United States. According to CBTRUS, the incidence of oligodendrogliomas, including anaplastic oligodendrogliomas, is approximately 0.3 per 100,000 persons. Depending on the study, these tumors account for 4% to 15% of intracranial gliomas. Based on this data, it appears that these are rare tumors.

Last updated on 05-01-20

Name: American Brain Tumor Association 8550 W. Bryn Mawr Ave, Ste 550
Chicago, IL, 60631, United States
Phone: +1-773-577-8750 Toll Free: 1-800-886-2282 Fax : +1-773-577-8738 Email: info@abta.org Url: https://www.abta.org/

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The RareGuru disease database is regularly updated using data generously provided by GARD, the United States Genetic and Rare Disease Information Center.

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