Mitochondrial complex III deficiency

Where is mitochondrial complex III located in the body?

Our bodies are made of many cells, small sphere-like units that collectively form every organ and body part. Each cell contains many, very small structures called mitochondria that produce energy for the cell. Inside each mitochondria, there are tiny chemicals called proteins which interact with each other. Complex III is the name of a group of proteins that work together inside the mitochondria. So, there are many complex III proteins in every mitochondria, many mitochondria in every cell, and many cells in the body.

Last updated on 05-01-20

What is the function of mitochondrial complex III?

Mitochondrial complex III works with other chemicals (called proteins) in the mitochondria to make energy for the cells in the body. The specific job of complex III is to act as a kind of pump, moving small molecules from one compartment of the mitochondria to another.

Last updated on 05-01-20

In-Depth Information

GeneReviews - Mitochondrial Disorders

GeneReviews provides a current, expert-authored, peer-reviewed, full-text article on mitochondrial disorders. GeneReview articles describe the application of genetic testing to the diagnosis, management, and genetic counseling of patients with specific inherited conditions.

Last updated on 04-27-20

Name: United Mitochondrial Disease Foundation 8085 Saltsburg Road, Suite 201
Pittsburgh, PA, 15239 , United States
Phone: +1-412-793-8077 Toll Free: 1-888-317-8633 Fax : +1-412-793-6477 Email: Url:
Name: The Mitochondria Research and Medicine Society PO Box 55322
Birmingham, AL,
Phone: 716-907-4349 Fax : 716-845-1047 Email: Url:
Name: MitoAction PO Box 51474
Boston, MA, 02205, United States
Phone: 1-888-MITO-411 (648-6411) for support line Toll Free: 1-888-648-6228 Email: Url:
Name: Muscular Dystrophy Association MDA 222 S Riverside Plaza Suite 1500
Chicago, IL, 60606, United States
Toll Free: 1-833-275-6321 (Helpline) Email: Url:

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