Malignant Atrophic Papulosis

What causes Degos disease?

Currently the cause of Degos disease is not known. Similar skin macules have been described in people with systemic lupus erythematosus and in a patient without lupus who had anticardiolipin antibodies and lupus anticoagulant.

Last updated on 05-01-20

What is the typical prognosis (long term outlook) for people with Degos disease?

Prognosis of individuals with Degos disease varies considerably depending on the extent of blood vessel involvement. Individuals with isolated skin macules have a good prognosis, while individuals with multisystem disease often face life threatening complications. To learn more about your or your loved one’s prognosis we strongly recommend that you speak with a healthcare provider.

Last updated on 05-01-20

How might Degos disease be treated?

Currently, there is not a targeted therapy for Degos disease that has been proven effective. Treatment of Degos disease has been attempted with antithrombotic agents, such as aspirin and dipyridamole. These treatments were reported to be effective in some patients. Other treatments that have been tried, but have shown inconsistent results, include anticoagulants and fibrinolytic agents (drugs to help break-up and dissolve clots), ticlopidine, pentoxifylline, prostaglandin E1, and interferon alpha-2a. Treatment with intravenous immunoglobulin has also been tried, but produced conflicting results. Infliximab was reported to be ineffective in one case. Immunosuppressives such as corticosteroids may worsen Degos disease.

For further information on your treatment options, we encourage you to discuss your questions and this information with your healthcare provider.

Last updated on 05-01-20

Social Networking Websites

Degos disease

The Degos Disease Support Network Patient Forum is a online community for people with Degos disease and their families. You may need to register to post on the forum, but registration is free. Click on Degos Disease Support Network Patient Forum to learn more.

Last updated on 04-27-20

Name: The Degos Disease Support Network Web site Email: http://www.degosdisease.com/contact Url: http://www.degosdisease.com/
Name: Steffens Scleroderma Foundation PO Box 38037
Albany, NY, 12203,
Url: http://www.steffens-scleroderma.org/

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