Kimura disease

What is the cause of Kimura disease?

The cause of Kimura disease is unknown, but it appears to be due to an abnormal immune response.

Last updated on 05-01-20

How is Kimura disease diagnosed?

Kimura disease can be diagnosed by a surgical biopsy. Diagnosis is important because Kimura disease can look like other more serious conditions such as other immune system disorders, drug reactions, infections, or specific types of cancer.

Last updated on 05-01-20

What is the long-term outlook for people with Kimura disease?

Individuals with Kimura disease should be followed to watch for the recurrence of the masses and for kidney disease. Kimura disease has not been associated with cancer or an increased risk for cancer. Masses are not painful or associated with other symptoms, but they can significantly affect the appearance of the face and neck or cause dental issues.

Last updated on 05-01-20

How many people have Kimura disease?

Kimura disease occurs most often in adults of Asian descent, but can occur in any ethnic group. It affects men more than women, and is rare in childhood. The exact incidence is unknown.

Last updated on 05-01-20

How might Kimura disease be treated?

There is no cure for Kimura disease, but surgery or medications can be used to remove or shrink the masses. Surgery followed by low dose radiation therapy appears to be the treatment resulting in the longest period of remission. Radiation therapy alone has also been used to treat the masses seen in Kimura disease. Steroids (such as prednisone), taken by mouth or via an injection in the skin, can shrink the masses but the mass often reappears after treatment is stopped. Steroids can also be used to treat the kidney disease. Other, less common, treatments include medications that decrease swelling and increase blood flow (such as oral pentoxifylline), medications that suppress the immune system (such as cyclosporine), radiotherapy, and a combination of several medications and steroids.

Last updated on 05-01-20


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The RareGuru disease database is regularly updated using data generously provided by GARD, the United States Genetic and Rare Disease Information Center.

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