Desmoplastic infantile ganglioglioma

How are desmoplastic infantile gangliomas diagnosed?

In addition to detecting the signs and symptoms commonly seen in DIGs, head CT scans and MRIs may reveal the presence of this type of brain tumor.

Last updated on 05-01-20

What is desmoplastic infantile gangliomas (DIGs)?

Desmoplastic infantile gangliomas (DIGs) are rare brain tumors that are normally located in the frontal or parietal lobes of the brain. They are usually diagnosed before 18 months of age with most infants presenting with a short duration of symptoms. Although seizures are not commonly observed, a bulging fontanelle, rapid head growth, vomiting, and a sunset sign are usually noted. The standard treatment for DIGs is surgical resection (surgical procedure in which the portion of the brain with the tumor is removed).

Last updated on 05-01-20

What prognosis is associated with desmoplastic infantile gangliogliomas?

Follow-up has generally been favorable following complete surgical resection in the reported cases of DIGs. Spontaneous regression of the tumor following partial surgical resection has also been documented.

Last updated on 05-01-20

What treatment is available for desmoplastic infantile gangliomas?

Surgical resection (removal of the area of the brain with the tumor) has been the standard treatment reported in the medical literature. The size of the resection is probably based on the size of the tumor, although the extent of the resection is not documented for all cases reported in the medical literature. Adjuvant therapy is generally not performed when a gross total resection can be performed. When total resection is not possible, some of suggested chemotherapy, as the effects of radiation on extremely young children may be harmful.

Last updated on 05-01-20

Where To Start

Desmoplastic Infantile Ganglioma

Cancer.Net, oncologist-approved cancer information from the American Society of Clinical Oncology, provides information about desmoplastic infantile ganglioma. Click on the link to read this information.

Last updated on 04-27-20

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