Acquired angioedema

What is the long-term outlook for people with acquired angioedema?

The long-term outlook (prognosis) can vary, and in most cases, it depends on whether an underlying disease is present. People who are treated for an underlying disease may see improvement or disappearance of symptoms, but sometimes this is only temporary.

The most severe complication of AAE is being deprived of oxygen (asphyxiation) due to significant edema of the upper airway, if this occurs. This can be life-threatening. People with AAE should understand what steps to take in order to get emergency treatment in the case of airway involvement. Because AAE is a rare disorder, few emergency department providers are familiar with its treatment. It may be helpful to remain equipped with a document that briefly explains the diagnosis and outlines the treatment for acute attacks.

Compared with the general population, people with AAE have a higher chance to develop B-cell lymphomas.

Last updated on 05-01-20

Name: US Hereditary Angioedema Association, Inc. Seven Waterfront Plaza 500 Ala Moana Blvd., Suite 400
Honolulu, HI, 96813, United States
Phone: 866-798-5598 Email: Url:

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The RareGuru disease database is regularly updated using data generously provided by GARD, the United States Genetic and Rare Disease Information Center.

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